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Institute of Metabolic Disease at Baylor Research Institute
Organic Acids Included in Quantitative Urine Organic Acids Test
Glyoxylic 2-Methylbutyrylglycine
Pyruvic Adipic
2-Oxoisovaleric Isovalerylglycine
Acetoacetic 5-Oxoproline
2-Oxo-3-methylvaleric 2-Hydroxyphenylacetic
2-Methylacetoacetic 3-Methyladipic
2-Oxoisocaproic Mevalonic
2-Oxoglutaric or alpha-ketoglutaric 3-Methylcrotonylglycine
Phenylpyruvic 2-Hydroxyglutaric
2-Oxoadipic 3-Hydroxyglutaric
4-Hydroxyphenylpyruvic Tiglylglycine
Succinylcetone Phenyllactic
Lactic 3-Hydroxy-3methylglutaric (HMG)
Glycolic Pimelic
2-Hydroxybutyric 4-Hydroxycyclohexylacetic
3-Hydroxypropionic Hexanoylglycine
3-Hydroxyisobutyric 4-Hydroxyphenylacetic
3-Hydroxybutyric 3-Hydroxydecanoic
2-Hydroxyisovaleric Lauric
2-Methyl-3-hydroxybutyric N-Acetylasparatic
3-Hydroxyisovaleric 2-Hydroxyadipic
Methylmalonic (MMA) 5-Hydroxymethyluracil
2-Hydroxyisocaproic 3-Hydroxyadipic
2-Ethyl-3-hydoxypropionic 3-Methylglutaconic
3-Hydroxyvaleric Suberic
4-Hydroxybutyric Orotic
2-Hydroxy-3-methylvaleric Glutaconic
Benzoic Aconitic
4-Hydroxyisovaleric Azelaic
Octanoic Isocitric
2-Methyl-3-hydroxyvaleric Citric
Ethylmalonic (EMA) 3-Hydroxydodecanoic
Phenylacetic Methylcitric
Succinic Hippuric
Methylsuccinic Myristic
Glyceric Sebacic
Uracil 4-Hydroxyphenyllactic
Fumaric Xanthine
5-Hydroxyhexanoic Phenylpropionylglycine
Thymine Palmitoleic
Glutaric 3-Hydroxytetradecanoic
Propionylglycine 2-Hydroxydecanedioic
Isobutyrylglycine Palmitic
Malonic 3-Hydroxydecanedioic
3-MethylGlutaric N-Acetyltyrosine
cis-4-Decenoic 3-Hydroxyhexadecanoic
Decanoic Linoleic
3-Hydroxyoctanoic Oleic
Butyrylglycine Stearic
Malic Suberylglycine