| Organic Acids Included in Quantitative Urine Organic Acids Test |
| Glyoxylic |
2-Methylbutyrylglycine |
| Pyruvic |
Adipic |
| 2-Oxoisovaleric |
Isovalerylglycine |
| Acetoacetic |
5-Oxoproline |
| 2-Oxo-3-methylvaleric |
2-Hydroxyphenylacetic |
| 2-Methylacetoacetic |
3-Methyladipic |
| 2-Oxoisocaproic |
Mevalonic |
| 2-Oxoglutaric or alpha-ketoglutaric |
3-Methylcrotonylglycine |
| Phenylpyruvic |
2-Hydroxyglutaric |
| 2-Oxoadipic |
3-Hydroxyglutaric |
| 4-Hydroxyphenylpyruvic |
Tiglylglycine |
| Succinylcetone |
Phenyllactic |
| Lactic |
3-Hydroxy-3methylglutaric (HMG) |
| Glycolic |
Pimelic |
| 2-Hydroxybutyric |
4-Hydroxycyclohexylacetic |
| 3-Hydroxypropionic |
Hexanoylglycine |
| 3-Hydroxyisobutyric |
4-Hydroxyphenylacetic |
| 3-Hydroxybutyric |
3-Hydroxydecanoic |
| 2-Hydroxyisovaleric |
Lauric |
| 2-Methyl-3-hydroxybutyric |
N-Acetylasparatic |
| 3-Hydroxyisovaleric |
2-Hydroxyadipic |
| Methylmalonic (MMA) |
5-Hydroxymethyluracil |
| 2-Hydroxyisocaproic |
3-Hydroxyadipic |
| 2-Ethyl-3-hydoxypropionic |
3-Methylglutaconic |
| 3-Hydroxyvaleric |
Suberic |
| 4-Hydroxybutyric |
Orotic |
| 2-Hydroxy-3-methylvaleric |
Glutaconic |
| Benzoic |
Aconitic |
| 4-Hydroxyisovaleric |
Azelaic |
| Octanoic |
Isocitric |
| 2-Methyl-3-hydroxyvaleric |
Citric |
| Ethylmalonic (EMA) |
3-Hydroxydodecanoic |
| Phenylacetic |
Methylcitric |
| Succinic |
Hippuric |
| Methylsuccinic |
Myristic |
| Glyceric |
Sebacic |
| Uracil |
4-Hydroxyphenyllactic |
| Fumaric |
Xanthine |
| 5-Hydroxyhexanoic |
Phenylpropionylglycine |
| Thymine |
Palmitoleic |
| Glutaric |
3-Hydroxytetradecanoic |
| Propionylglycine |
2-Hydroxydecanedioic |
| Isobutyrylglycine |
Palmitic |
| Malonic |
3-Hydroxydecanedioic |
| 3-MethylGlutaric |
N-Acetyltyrosine |
| cis-4-Decenoic |
3-Hydroxyhexadecanoic |
| Decanoic |
Linoleic |
| 3-Hydroxyoctanoic |
Oleic |
| Butyrylglycine |
Stearic |
| Malic |
Suberylglycine |