Quantitative urine organic acid analysis is useful for evaluation and monitoring organic acidemias and fatty acid oxidation disorders. Our methodology includes analysis for succinylacetone, orotic acid, glutaric acid, methylmalonic acid, methylcitric, N-acetylasparatic, mevalonic acid and several acylglycines.
Quantitative results for 100 organic acids (see table below) with age related references ranges and interpretations are included in the test report.
Download Test Requisition
Department: Mass Spectrometry
Methodology: Silicic Acid Extraction with Gas Chromatography/Mass Spectrometry
Sample:
Urine (random collection)
Optimal sample volume - 5 mL. Minimum sample volume – 2 mL.
Collect urine in a sterile container with no preservatives.
Shipping/Handling: Freeze urine and ship overnight on 3-4 lbs of dry ice using a guaranteed overnight courier.
CPT code: 83918
Turnaround Time: 3-7 working days from sample receipt.
|
Organic Acids Included in Quantitative Urine Organic Acids Test |
|
Glyoxylic |
2-Methylbutyrylglycine |
|
Pyruvic |
Adipic |
|
2-Oxoisovaleric |
Isovalerylglycine |
|
Acetoacetic |
5-Oxoproline |
|
2-Oxo-3-methylvaleric |
2-Hydroxyphenylacetic |
|
2-Methylacetoacetic |
3-Methyladipic |
|
2-Oxoisocaproic |
Mevalonic |
|
2-Oxoglutaric or alpha-ketoglutaric |
3-Methylcrotonylglycine |
|
Phenylpyruvic |
2-Hydroxyglutaric |
|
2-Oxoadipic |
3-Hydroxyglutaric |
|
4-Hydroxyphenylpyruvic |
Tiglylglycine |
|
Succinylcetone |
Phenyllactic |
|
Lactic |
3-Hydroxy-3methylglutaric (HMG) |
|
Glycolic |
Pimelic |
|
2-Hydroxybutyric |
4-Hydroxycyclohexylacetic |
|
3-Hydroxypropionic |
Hexanoylglycine |
|
3-Hydroxyisobutyric |
4-Hydroxyphenylacetic |
|
3-Hydroxybutyric |
3-Hydroxydecanoic |
|
2-Hydroxyisovaleric |
Lauric |
|
2-Methyl-3-hydroxybutyric |
N-Acetylasparatic |
|
3-Hydroxyisovaleric |
2-Hydroxyadipic |
|
Methylmalonic (MMA) |
5-Hydroxymethyluracil |
|
2-Hydroxyisocaproic |
3-Hydroxyadipic |
|
2-Ethyl-3-hydoxypropionic |
3-Methylglutaconic |
|
3-Hydroxyvaleric |
Suberic |
|
4-Hydroxybutyric |
Orotic |
|
2-Hydroxy-3-methylvaleric |
Glutaconic |
|
Benzoic |
Aconitic |
|
4-Hydroxyisovaleric |
Azelaic |
|
Octanoic |
Isocitric |
|
2-Methyl-3-hydroxyvaleric |
Citric |
|
Ethylmalonic (EMA) |
3-Hydroxydodecanoic |
|
Phenylacetic |
Methylcitric |
|
Succinic |
Hippuric |
|
Methylsuccinic |
Myristic |
|
Glyceric |
Sebacic |
|
Uracil |
4-Hydroxyphenyllactic |
|
Fumaric |
Xanthine |
|
5-Hydroxyhexanoic |
Phenylpropionylglycine |
|
Thymine |
Palmitoleic |
|
Glutaric |
3-Hydroxytetradecanoic |
|
Propionylglycine |
2-Hydroxydecanedioic |
|
Isobutyrylglycine |
Palmitic |
|
Malonic |
3-Hydroxydecanedioic |
|
3-MethylGlutaric |
N-Acetyltyrosine |
|
cis-4-Decenoic |
3-Hydroxyhexadecanoic |
|
Decanoic |
Linoleic |
|
3-Hydroxyoctanoic |
Oleic |
|
Butyrylglycine |
Stearic |
|
Malic |
Suberylglycine |